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Educational Series in Congenital Heart Disease Congenital left-sided heart obstruction

Echo Research & Practice volume 5, pages R23–R36 (2018)Cite this article

Abstract

Congenital obstruction of the left ventricular outflow tract remains a significant problem and multilevel obstruction can often coexist. Obstruction can take several morphological forms and may involve the subvalvar, valvar or supravalvar portion of the aortic valve complex. Congenital valvar stenosis presenting in the neonatal period represents a spectrum of disorders ranging from the hypoplastic left heart syndrome to almost normal hearts. Treatment options vary dependent on the severity of the left ventricular outflow tract obstruction (LVOTO) and the variable degree of left ventricular hypoplasia as well as the associated lesions such as arch hypoplasia and coarctation.

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  1. Great Ormond Street Hospital for Children NHS Foundation Trust, London, UK

    Michelle Carr MB BCh BAO & Jan Marek MD PhD FESC

  2. Bristol Heart Institute, University Hospitals Bristol, Bristol, UK

    Stephanie Curtis BSc (Hons) MB ChB MD FRCP FESC

  3. Institute of Cardiovascular Sciences, University College London, London, UK

    Jan Marek MD PhD FESC

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  1. Michelle Carr MB BCh BAO
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Correspondence to Stephanie Curtis BSc (Hons) MB ChB MD FRCP FESC.

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Carr, M., Curtis, S. & Marek, J. Educational Series in Congenital Heart Disease Congenital left-sided heart obstruction. Echo Res Pract 5, R23–R36 (2018). https://doiorg.publicaciones.saludcastillayleon.es/10.1530/ERP-18-0016

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